Mounier-Kuhn Syndrome, also known as tracheobronchmegaly, is a rare disease characterized by a noticeable enlargement of the trachea and main bronchi.

Although the cause of Mounier-Kuhn is unknown, it is believed the disease is due to an absence of smooth muscle and elastic connective tissue in the trachea
and main bronchi. This condition allows the trachea and main bronchi to become flaccid and collapse on expiration or cough.

The dynamics of this irregular airway predisposes a person to recurrent respiratory tract infections, pneumonia, bronchiectasis, emphysema and pulmonary fibrosis.

Mounier-Kuhn can cause progressive pulmonary disease leading to respiratory failure and death. Most cases of Mounier- Kuhn present in adult life, typically
in the third decade or later. This disease, however, has been diagnosed in children as young as fifteen (15) months old.

There is much to be learned about the cause and treatment for Mounier-Kuhn Syndrome. The Just Breathe Foundaton plans on helping to further education
and research for this disease.

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